Citations 1
Scoliosis in Fibrodysplasia Ossificans Progressiva
Elsabbagh, Zaid , Cha, Myung-Jin , Pignolo, Robert J. , Fs, Kaplan, Sponseller, Paul D., Kaplan, Frederick S. , Sponseller, Paul D. , Kaplan, Frederick S , Sponseller, Paul D
JBJS Case Connector | February 5, 2026 | Volume: 16 | Issue: 1 | Pages: No page available
Case: Fibrodysplasia ossificans progressiva (FOP) is a rare genetic disorder characterized by progressive heterotopic ossification. Scoliosis may develop and progress rapidly, especially during adolescence. We report 4 patients with FOP and scoliosis during early adolescence: A 12-year-old girl underwent T4-S2 posterior spinal fusion (PSF); another 12-year-old girl underwent T4-S2 PSF; a 13-year-old boy underwent T3-L4 PSF; and a 14-year-old girl was managed nonoperatively because the complex deformity and ankylosed shoulders could not be adequately balanced with surgery. Conclusion: In patients with FOP, surgical intervention can reduce thoracic deformity and improve pulmonary function but carries substantial risks, including heterotopic ossification.